Despite their heterogeneity, small island developing states (SIDS) are recognized as being particularly at risk to climate change, and, as they share numerous common traits, the United Nations recognizes them as a special group. SIDS have been quite vocal in calling attention to the challenges they face from climate change and advocating for greater international ambition to limit global warming. Here, we unpack factors that are helpful in understanding the relationship between climate change and SIDS through a review of studies that span disciplines and methodologies. We assess patterns of hazards, exposure, and vulnerability; impacts and risks; awareness and knowledge; adaptation planning and implementation; mitigation; loss and damage; and climate justice to provide an overarching review of literature on climate change and SIDS.